Pushing the limit on laminopathies
Abstract
Mutations in lamins in skeletal muscle cells have been shown to reduce nuclear stability, increase nuclear envelope rupture, and induce DNA damage and cell death. New research shows that limiting mechanical loads can rescue myofibre function and viability.
- Publication:
-
Nature Materials
- Pub Date:
- March 2020
- DOI:
- 10.1038/s41563-020-0648-1
- Bibcode:
- 2020NatMa..19..378E